Isolated bone marrow mastocytosis: an underestimated subvariant of indolent systemic mastocytosis.

نویسندگان

  • Roberta Zanotti
  • Patrizia Bonadonna
  • Massimiliano Bonifacio
  • Anna Artuso
  • Donatella Schena
  • Maurizio Rossini
  • Omar Perbellini
  • Sabrina Colarossi
  • Marco Chilosi
  • Giovanni Pizzolo
چکیده

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Skeletal implications of isolated bone marrow mastocytosis.

In the article on the isolated bone marrow mastocytosis (IBMM) as an underestimated subvariant of indolent systemic mastocytosis (ISM), Zanotti et al. reported that 54.7% of patients with unexplained/recurrent anaphylaxis or severe allergic reactions were found to be suffering from IBMM. They conclude that the incidence of IBMM can be frequently underestimated, especially in the face of a lack ...

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Biochemical markers predictive for bone marrow involvement in systemic mastocytosis.

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Indolent systemic mastocytosis limited to the bone: a case report and review of the literature.

CONTEXT Systemic mastocytosis is defined as a clonal disorder of mast cells and their precursor cells and is currently classified as a myeloproliferative neoplasm. Its clinical course has a wide spectrum, ranging from indolent disease, with normal life expectancy, to highly aggressive disease, associated with multisystemic involvement and poor overall survival. The aim of this study was to repo...

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Systemic mastocytosis (SM) is a rare clonal disorder of mast cells that can range from chronic smouldering type to aggressive mast cell leukaemia. It presents with non-specific symptoms like urticaria pigmentosa, unexplained flushing, hypotension and abdominal cramps, which may lead to a misdiagnosis, if there is no high index of clinical suspicion. This is a case report of a 52-year-old lady, ...

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عنوان ژورنال:
  • Haematologica

دوره 96 3  شماره 

صفحات  -

تاریخ انتشار 2011